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Table 1 Baseline characteristics of 81 PHID patients, ALTADIH Cohort, 2007-2010

From: T-cell activation discriminates subclasses of symptomatic primary humoral immunodeficiency diseases in adults

Characteristics

Distribution

Sociodemographic data

  

     Female, n (%)

48

(59)

     Median age at diagnosis in years (interquartile range)

41 (35–54)

     Median age at enrolment in years (interquartile range)

46 (38–58)

Clinical data, n (%)

  

Respiratory tract infections

  

     Otitis, sinusitis, nasopharyngitis, polyposis

64

(79)

     Bronchitis, pneumonia

65

(80)

     Bronchiectasis

21

(26)

Gastrointestinal tract infection

  

     Chronic diarrhea

16

(20)

     Acute diarrhea

13

(16)

     Lambliasis

11

(14)

PHID complications: at least one of the following

31

(38)

     Lymphoid hyperplasia

16

(20)

     Splenomegaly

14

(17)

     Autoimmune manifestations*

14

(17)

     Granulomatous disease

9

(11)

     Villous atrophy

5

(6)

     Chronic inflammatory intestinal disease

4

(5)

Therapeutic data, n (%)

  

Subcutaneous or intravenous immunoglobulin substitution

66

(81)

  1. *Autoimmune anemia, autoimmune neutropenia, autoimmune thrombocytopenia, Hashimoto thyroiditis, Goujerot-Sjögren syndrome.
  2. Location of biopsy proven granuloma: lymph node, digestive tract, spleen, bone narrow.