Characteristics | Distribution | |
---|---|---|
Sociodemographic data | ||
Female, n (%) | 48 | (59) |
Median age at diagnosis in years (interquartile range) | 41 (35–54) | |
Median age at enrolment in years (interquartile range) | 46 (38–58) | |
Clinical data, n (%) | ||
Respiratory tract infections | ||
Otitis, sinusitis, nasopharyngitis, polyposis | 64 | (79) |
Bronchitis, pneumonia | 65 | (80) |
Bronchiectasis | 21 | (26) |
Gastrointestinal tract infection | ||
Chronic diarrhea | 16 | (20) |
Acute diarrhea | 13 | (16) |
Lambliasis | 11 | (14) |
PHID complications: at least one of the following | 31 | (38) |
Lymphoid hyperplasia | 16 | (20) |
Splenomegaly | 14 | (17) |
Autoimmune manifestations* | 14 | (17) |
Granulomatous disease† | 9 | (11) |
Villous atrophy | 5 | (6) |
Chronic inflammatory intestinal disease | 4 | (5) |
Therapeutic data, n (%) | ||
Subcutaneous or intravenous immunoglobulin substitution | 66 | (81) |