Restituted seruma Patient no. | CP | LPc | AP |
---|
1 | +++b | ± | +++ |
2 | +++ | - | +++ |
3 | +++ | ± | +++ |
4 | +++ | + | +++ |
5 | +++ | ++ | +++ |
6 | +++ | - | +++ |
- arhC2 was added to C2-deficient serum, final concentration 25 μg/ml.
- bComplement activation tested by ELISA. +++ = 100% activation, ++ = 50%, + = 20%, - = no activation.
- cLP activity reflects the MBL concentration governed by MBL genotype. Patient 5 is homozygous for the wild-type structural gene variant (genotype A/A), while the other patients are heterozygous for this allele.